PubMed journal article [Idiopathic pulmonary hemosiderosis were found in PRIME PubMed. Download Source. Revista chilena de pediatría pg PubMed journal article [Idiopathic pulmonary hemosiderosis: review of literature and case report were found in La Pediatria Sep 30 pg Revista Cubana de Pediatría Idiopathic pulmonary hemosiderosis is those processes characterized by anomalous depots of hemosiderin in the pulmonary.
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Idiopathic pulmonary hemosiderosis
Long-term outcome of idiopathic pulmonary hemosiderosis in children. A 4 year-old boy with a previous history of recurrent wheezing, with no criteria of severity and no associated hmosiderosis, was observed in an emergency department for fever, vomiting and prostration. As such, given the iron-deficiency anemia with characteristics compatible with blood loss although not identifiedand despite the absence of respiratory symptoms at this phase, we started looking for other sources of hemorrhage, namely pulmonary.
The prognosis of idiopathic PH tends to improve with age and is more favorable when the diagnosis is made before the progression to pulmonary fibrosis. Idiopathic pulmonary hemosiderosis in adults: There are no universal recommendations regarding treatment of idiopathic PH. The child is currently asymptomatic, with Hb levels between Orphanet J Rare Dis. Severe respiratory distress in a child with pulmonary idiopathic hemosiderosis initially presenting with iron-deficiency anemia.
We present the case of a 4 pediatira child presenting with fever, vomiting and prostration, associated with pallor.
Subsequently, pulmonary infiltrates suggestive of alveolar hemorrhage were observed in the chest radiography. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact. SCS Quadra 1, Bl. On the other hand, the rarity of the alveolar hemorrhage and the variability of the clinical course frequently result in a delay in the diagnosis.
J Clin Case Rep. The clinical spectrum is varied, and anemia may constitute the only manifestation of illness, preceding other signs and periatria by several months.
Services on Demand Journal. Anemia might be the only manifestation of PH, preceding any other symptom and sign by several months. Vitamin B 12 and folic acid were within normal range and the bone marrow smear was compatible with sideropenia.
Open in a separate window. Annals of Pediatrics is the Body of Scientific Expression of the Association and is the vehicle through which members communicate. To confirm alveolar hemorrhage, a fibrobronchoscopy was performed. After 3 days, he maintained fever and the chest radiograph showed a diffuse bilateral opacity with ill-defined edges, interpreted as an atypical pneumonia, and he was started on clarithromycin.
He was initiated on corticosteroid therapy, later associated to an immunosuppressive agent, with subsequent correction of anemia and of the radiological pattern. The Impact Factor measures the average number of citations received in a particular year by papers published in the journal during the two receding years.
The patient is currently asymptomatic. Diffuse alveolar hemorrhage is caused by loss of integrity of the basement membrane of pulmonary capillaries, with consequent leakage of blood into the alveolar space. A favorable prognosis may be expected in our case, as there were no major episodes of hemorrhage and response to therapy was favorable.
Hemosiderin-laden macrophages were also identified using Perls stain Figure 2confirming the diagnosis of PH. Idiopathic pulmonary hemosiderosis in an adult. He was transfused with packed red blood cells and readmitted. A physician survey reveals differences in management of idiopathic pulmonary hemosiderosis. Upper and lower gastrointestinal endoscopies with biopsies were performed and no hemorrhagic lesion was found, and the mucosa was macroscopically and histologically normal. After excluding the most frequent causes of PH: Idiopathic pulmonary hemosiderosis is a potentially fatal disease that results from episodes of alveolar hemorrhage of unknown origin.
Idiopathic pulmonary hemosiderosis treated with azathioprine in a child
Pediatr Rio de J. Pulmonary hemosiderosis PH is a rare disease that may occur at any age, although it generally affects children, with an estimated incidence of 0. Are you a health professional able to prescribe or dispense drugs? Journal List Einstein Sao Paulo v. Foi iniciado tratamento com oxacilina e azitromicina.
He had microcytic and hypochromic anemia refractory to iron therapy. Acute respiratory insufficiency as debut of idiopathic pulmonary hemosiderosis in an infant. Author information Article notes Copyright and License information Disclaimer.